A toddler with a rare disease that affects hearing and sight was tickled pink when a biker revved up the engine of a Harley Davidson at a motorbike show where she was guest of honour.

The magical moment was captured on video showing four-year-old Isabelle Gregory responding as Gaz Davies, parts and accessories advisor at Chester Harley Davidson, revs up the Harley Dyna Streetbob model.

Related story: Chester bikers' show to raise cash for brave little Isabelle

Isabelle and family, from Kingsway, had been invited along to the recent Route 41 Bike and Custom show at The Peacock Hotel in Christleton Road, Boughton.

Isabelle Gregory, four, from Kingsway, with mum and dad, Jemma and Craig and six-year-old brother Isaac with motoryclists from the Taliesin Brotherhood who organised the Route 41 Bike and Custom show at The Peacock Hotel in Christleton Road, Boughton, last month. Isabelle was guest of honour.

Mum Jemma, who has another daughter Imogen, three, and son Isaac, six, told The Chronicle beforehand how much Isabelle, who has life-limiting mitochondrial disease affecting brain function, simply loves the sound of bikes revving and is not at all scared.

A special competition category was even created called ‘Isabelle’s choice’ for Isabelle to select her favourite bike of the day with the help of her mum and dad, Jemma and Craig. Mum predicted it was likely to be the ‘noisiest one’ although in the event her brother had a hand in the choice of a mini moto machine.

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And the Chester chapter of the Taliesin Brotherhood who hosted the show have promised to use their skills to create a sensory garden at Isabelle’s home. They raised £1,200 on the day which will help pay for materials with any surplus going towards the charity SPACE – founded by Isabelle’s mum Jemma to support parents of children with additional needs.

Jemma Gregory with daughter Isabelle in the garden of their Kingsway home.

Harley Davidson spokesman Gemma Macey said: “The guy revving the bike is Gaz Davies – parts and accessories advisor at Chester Harley Davidson. He took a shine to Izzy and she certainly made everyone’s day! Izzy is such a special little girl and we think it’s great that she and her mum’s charity is gaining great publicity so we are more than happy to help.”

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Harley Davidson Chester is holding an open weekend this Saturday and Sunday (May 21 and 22) with bikes, bands, tattoo and graffiti artists, demonstrations of custom paint jobs and refreshments.

For more information visit their website, their Facebook page and Twitter account.